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產(chǎn)品詳情
  • 產(chǎn)品名稱:Anti-Ataxin 7抗體

  • 產(chǎn)品型號(hào):脊髓小腦共濟(jì)失調(diào)蛋白7抗體
  • 產(chǎn)品廠商:KALANG
  • 產(chǎn)品文檔:
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簡單介紹:
Anti-Ataxin 7抗體產(chǎn)品質(zhì)量穩(wěn)定,實(shí)驗(yàn)效果明顯,貨期快,價(jià)格優(yōu)惠,歡迎垂詢訂購!我公司長期供應(yīng)**組化抗體、WB抗體、**組化試劑盒和抗體試驗(yàn)所需全部相關(guān)試劑、熒光標(biāo)記抗體、單克隆抗體、多克隆抗體、各種標(biāo)記的二抗IgG/IgM/IgD/IgA等科研實(shí)驗(yàn)抗體。Anti-Ataxin 7抗體用于**組化實(shí)驗(yàn),WB實(shí)驗(yàn),相應(yīng)的標(biāo)記抗體有HRP標(biāo)記抗體,FITC標(biāo)記,BIO等。
詳情介紹:
Rabbit  Anti-Ataxin 7
Cat. Number:
Anti-Ataxin 7抗體KL-11318R
Quantity size:
0.2ml
Concentration:
1mg/ml   Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
The human ataxin-7 gene, also known as spinocerebellar ataxia 7 or SCA7, maps to chromosome 3p13-p12, has a 2,727-bp open reading frame, and encodes a 892 amino acid protein containing a nuclear localization signal Anti-Ataxin 7抗體and a polyglutamine tract (1,2). SCA7 is an autosomal dominant neurodegenerative disorder characterized by ataxia and selective neuronal cell loss caused by the expansion of a translated CAG repeat encoding a polyglutamine tract in ataxin-7, which is the SCA7 gene product (3,4). Ataxin-7 is expressed within neurons both affected and unaffected in SCA7 pathology with subcellular localization being variable depending upon the neuronal subtype (5). Polyglutamine expanded in ataxin-7 may carry out its pathogenic effects in the nucleus by altering the matrix-associated nuclear structure and/or by disrupting nucleolar function (6).
Also known as:
Ataxin7; Ataxin-7; ADCAII; ATXN 7; OPCA III; OPCA3; SCA 7; SCA7; Spinocerebellar Ataxia 7; Spinocerebellar ataxia type Anti-Ataxin 7抗體7 protein; ATX7_HUMAN.
Specificity:
Rabbit Polyclonal IgG, affinity purified by Protein A.
Reacts with: Human, Mouse, Rat, Dog, Pig, Cow, Horse, Rabbit, Sheep, .
Immunogen: KLH conjugated synthetic peptide derived from human Ataxin 7.
Predicted Molecular Weight: 95kDa.
Storage:
Shipped at 4℃, Anti-Ataxin 7抗體Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  ICC=1:100-500  IF=1:100-500   
Not yet tested in other applications. 
Optimal working Anti-Ataxin 7抗體dilutions must be determined by the end user.
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kl142Mu01 細(xì)胞間粘附分子5(ICAM5)多克隆抗體 Polyclonal Antibody to Intercellular Adhesion Molecule 5 (ICAM5)
kl142Rb51 細(xì)胞間粘附分子5(ICAM5)多克隆抗體 Polyclonal Antibody to Intercellular Adhesion Molecule 5 (ICAM5)
kl143Ca01 血管內(nèi)皮生長因子A(VEGFA)多克隆抗體 Polyclonal Antibody to Vascular Endothelial Growth Factor A (VEGFA)
kl143Eq01 血管內(nèi)皮生長因子A(VEGFA)多克隆抗體 Polyclonal Antibody to Vascular Endothelial Growth Factor A (VEGFA)
kl143Ga01 血管內(nèi)皮生長因子A(VEGFA)多克隆抗體 Polyclonal Antibody to Vascular Endothelial Growth Factor A (VEGFA)
kl143Po01 血管內(nèi)皮生長因子A(VEGFA)多克隆抗體 Polyclonal Antibody to Vascular Endothelial Growth Factor A (VEGFA)
kl144Bo01 血管內(nèi)皮生長因子B(VEGFB)多克隆抗體 Polyclonal Antibody to Vascular Endothelial Growth Factor B (VEGFB)
kl145Bo01 血管內(nèi)皮生長因子C(VEGFC)多克隆抗體 Polyclonal Antibody to Vascular Endothelial Growth Factor C (VEGFC)
kl146Bo01 血管內(nèi)皮生長因子D(VEGFD)多克隆抗體 Polyclonal Antibody to Vascular Endothelial Growth Factor D (VEGFD)
kl147Bo01 脂聯(lián)素受體1(ADIPOR1)多克隆抗體 Polyclonal Antibody to Adiponectin Receptor 1 (ADIPOR1)
kl147Ga01 脂聯(lián)素受體1(ADIPOR1)多克隆抗體 Polyclonal Antibody to Adiponectin Receptor 1 (ADIPOR1)
kl147Hu01 脂聯(lián)素受體1(ADIPOR1)多克隆抗體 Polyclonal Antibody to Adiponectin Receptor 1 (ADIPOR1)
kl147Mu01 脂聯(lián)素受體1(ADIPOR1)多克隆抗體 Polyclonal Antibody to Adiponectin Receptor 1 (ADIPOR1)

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