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產品詳情
  • 產品名稱:Anti-BBS2抗體

  • 產品型號:巴爾得-別德爾綜合征相關蛋白2抗體
  • 產品廠商:KALANG
  • 產品文檔:
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簡單介紹:
Anti-BBS2抗體產品質量穩定,實驗效果明顯,貨期快,價格優惠,歡迎垂詢訂購!我公司長期供應**組化抗體、WB抗體、**組化試劑盒和抗體試驗所需全部相關試劑、熒光標記抗體、單克隆抗體、多克隆抗體、各種標記的二抗IgG/IgM/IgD/IgA等科研實驗抗體。Anti-BBS2抗體用于**組化實驗,WB實驗,相應的標記抗體有HRP標記抗體,FITC標記,BIO等。
詳情介紹:
Rabbit  Anti-BBS2
Cat. Number:
Anti-BBS2抗體KL-11506R
Quantity size:
0.2ml
Concentration:
1mg/ml   Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
Bardet-Biedl syndrome Anti-BBS2抗體(BBS) is a pleiotropic genetic disorder characterized by obesity, photoreceptor degeneration, polydactyly, hypogenitalism, renal abnormalities, and developmental delay. Other associated clinical findings in BBS patients include diabetes, hypertension, and congenital heart defects. BBS is a heterogeneous disorder that maps to eight genetic loci and encodes eight proteins, BBS1-BBS8. Five BBS genes encode basal body or cilia proteins, suggesting that BBS is a ciliary dysfunction disorder. BBS2 is a 721-amino acid protein that is evolutionarily conserved and is expressed in a broad range of tissues including: brain, kidney, adrenal gland, and thyroid gland. Loss of BBS2 may be involved in defects in social interactions as well as infertility. BBS2 retinopathy involves normal retina development followed by apoptotic death of photoreceptors, the primary ciliated cells of the retina.Anti-BBS2抗體
Also known as:
Bardet Biedl syndrome 2; Bardet Biedl syndrome 2 protein; BBS; MGC20703; BBS2_HUMAN.
Specificity:
Rabbit Polyclonal IgG, affinity purified by Protein A.Anti-BBS2抗體
Reacts with: Human, Mouse, Rat, Chicken, Dog, Horse, Rabbit, Sheep, .
Immunogen: KLH conjugated synthetic peptide derived from human BBS2.
Predicted Molecular Weight: 80kDa.
Storage:
Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  ICC=1:100-500  IF=1:100-500   
Not yet tested in other applications. 
Optimal working dilutions must be Anti-BBS2抗體determined by the end user.
kl439Hu01 蛋白激酶Cε(PKCε)多克隆抗體 Polyclonal Antibody to Protein Kinase C Epsilon (PKCe)
kl439Mu01 蛋白激酶Cε(PKCε)多克隆抗體 Polyclonal Antibody to Protein Kinase C Epsilon (PKCe)
kl442Hu01 阻抑素(PHB)多克隆抗體 Polyclonal Antibody to Prohibitin (PHB)
kl442Mu01 阻抑素(PHB)多克隆抗體 Polyclonal Antibody to Prohibitin (PHB)
kl442Ra01 阻抑素(PHB)多克隆抗體 Polyclonal Antibody to Prohibitin (PHB)
kl444Hu01 橋粒芯糖蛋白3(DSG3)多克隆抗體 Polyclonal Antibody to Desmoglein 3 (DSG3)
kl446Hu01 抑制素βC(INHβC)多克隆抗體 Polyclonal Antibody to Inhibin Beta C (INHbC)
kl446Ra01 抑制素βC(INHβC)多克隆抗體 Polyclonal Antibody to Inhibin Beta C (INHbC)
kl449Hu01 胱天蛋白酶7(CASP7)多克隆抗體 Polyclonal Antibody to Caskle 7 (CASP7)
kl449Mu01 胱天蛋白酶7(CASP7)多克隆抗體 Polyclonal Antibody to Caskle 7 (CASP7)
kl449Ra01 胱天蛋白酶7(CASP7)多克隆抗體 Polyclonal Antibody to Caskle 7 (CASP7)
kl450Hu01 激肽釋放酶4(KLK4)多克隆抗體 Polyclonal Antibody to Kallikrein 4 (KLK4)
kl450Mu01 激肽釋放酶4(KLK4)多克隆抗體 Polyclonal Antibody to Kallikrein 4 (KLK4)
kl450Ra01 激肽釋放酶4(KLK4)多克隆抗體 Polyclonal Antibody to Kallikrein 4 (KLK4)
kl451Hu01 激肽釋放酶5(KLK5)多克隆抗體 Polyclonal Antibody to Kallikrein 5 (KLK5)
kl451Mu01 激肽釋放酶5(KLK5)多克隆抗體 Polyclonal Antibody to Kallikrein 5 (KLK5)
kl457Hu01 胱天蛋白酶14(CASP14)多克隆抗體 Polyclonal Antibody to Caskle 14 (CASP14)
kl457Mu01 胱天蛋白酶14(CASP14)多克隆抗體 Polyclonal Antibody to Caskle 14 (CASP14)
kl457Ra01 胱天蛋白酶14(CASP14)多克隆抗體 Polyclonal Antibody to Caskle 14 (CASP14)
kl464Hu01 鹽皮質**受體(MR)多克隆抗體 Polyclonal Antibody to Mineralocorticoid Receptor (MR)
kl464Ra01 鹽皮質**受體(MR)多克隆抗體 Polyclonal Antibody to Mineralocorticoid Receptor (MR)

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