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產(chǎn)品詳情
  • 產(chǎn)品名稱:Anti-BBS7抗體

  • 產(chǎn)品型號:巴爾得-別德爾綜合征相關(guān)蛋白7抗體
  • 產(chǎn)品廠商:KALANG
  • 產(chǎn)品文檔:
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簡單介紹:
Anti-BBS7抗體產(chǎn)品質(zhì)量穩(wěn)定,實(shí)驗(yàn)效果明顯,貨期快,價(jià)格優(yōu)惠,歡迎垂詢訂購!我公司長期供應(yīng)**組化抗體、WB抗體、**組化試劑盒和抗體試驗(yàn)所需全部相關(guān)試劑、熒光標(biāo)記抗體、單克隆抗體、多克隆抗體、各種標(biāo)記的二抗IgG/IgM/IgD/IgA等科研實(shí)驗(yàn)抗體。Anti-BBS7抗體用于**組化實(shí)驗(yàn),WB實(shí)驗(yàn),相應(yīng)的標(biāo)記抗體有HRP標(biāo)記抗體,FITC標(biāo)記,BIO等。
詳情介紹:
Rabbit  Anti-BBS7
Cat. Number:
Anti-BBS7抗體KL-11509R
Quantity size:
0.2ml
Concentration:
1mg/ml   Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
Bardet-Biedl syndrome (BBS) is a pleiotropic genetic disorder characterized by obesity, photoreceptor degeneration,Anti-BBS7抗體 polydactyly, hypogenitalism, renal abnormalities, and developmental delay. BBS patients also have an increased risk of developing diabetes, hypertension, and congenital heart defects. BBS is a heterogeneous disorder mapping to eight genetic loci and encoding eight proteins, BBS1-BBS8. Five BBS proteins encode basal body or cilia proteins, suggesting that BBS is a ciliary dysfunction disorder. BBS2 contains two overlapping genes: BBS2L1 and BBS2L2. BBSL1 was re-named BBS7, whereas BBS2L2 independently funcitons as BBS1. BBS7 contains 672 amino acids and is expressed at low to moderate levels in most human tissues.Anti-BBS7抗體
Also known as:
Bardet-Biedl syndrome 7; Bardet-Biedl syndrome 7 protein; BBS2-like 1; BBS7_HUMAN.
Specificity:
Rabbit Polyclonal IgG, affinity purified by Protein A.Anti-BBS7抗體
Reacts with: Human, Mouse, Rat, Chicken, Dog, Pig, Cow, Horse, Rabbit, Sheep, .
Immunogen: KLH conjugated synthetic peptide derived from human BBS7.
Predicted Molecular Weight: 80kDa.
Storage:
Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  ICC=1:100-500  IF=1:100-500   
Not yet tested in other applications. 
Optimal working dilutions Anti-BBS7抗體must be determined by the end user.
kl524Hu01 組織因子(TF)多克隆抗體 Polyclonal Antibody to Tissue Factor (TF)
kl524Mu01 組織因子(TF)多克隆抗體 Polyclonal Antibody to Tissue Factor (TF)
kl524Po01 組織因子(TF)多克隆抗體 Polyclonal Antibody to Tissue Factor (TF)
kl524Ra01 組織因子(TF)多克隆抗體 Polyclonal Antibody to Tissue Factor (TF)
kl524Rb52 組織因子(TF)多克隆抗體 Polyclonal Antibody to Tissue Factor (TF)
kl525Hu01 組織型纖溶酶原激活因子(tPA)多克隆抗體 Polyclonal Antibody to Plasminogen Activator, Tissue (tPA)
kl525Mu01 組織型纖溶酶原激活因子(tPA)多克隆抗體 Polyclonal Antibody to Plasminogen Activator, Tissue (tPA)
kl525Po01 組織型纖溶酶原激活因子(tPA)多克隆抗體 Polyclonal Antibody to Plasminogen Activator, Tissue (tPA)
kl525Ra01 組織型纖溶酶原激活因子(tPA)多克隆抗體 Polyclonal Antibody to Plasminogen Activator, Tissue (tPA)
kl528Ra01 血小板衍生生長因子A(PDGFA)多克隆抗體 Polyclonal Antibody to Platelet Derived Growth Factor Subunit A (PDGFA)
kl528Rb51 血小板衍生生長因子A(PDGFA)多克隆抗體 Polyclonal Antibody to Platelet Derived Growth Factor Subunit A (PDGFA)
kl529Ca01 血栓調(diào)節(jié)蛋白(TM)多克隆抗體 Polyclonal Antibody to Thrombomodulin (TM)
kl529Hu01 血栓調(diào)節(jié)蛋白(TM)多克隆抗體 Polyclonal Antibody to Thrombomodulin (TM)
kl529Mu01 血栓調(diào)節(jié)蛋白(TM)多克隆抗體 Polyclonal Antibody to Thrombomodulin (TM)
kl529Po01 血栓調(diào)節(jié)蛋白(TM)多克隆抗體 Polyclonal Antibody to Thrombomodulin (TM)
kl529Ra01 血栓調(diào)節(jié)蛋白(TM)多克隆抗體 Polyclonal Antibody to Thrombomodulin (TM)
kl529Rb51 血栓調(diào)節(jié)蛋白(TM)多克隆抗體 Polyclonal Antibody to Thrombomodulin (TM)
kl531Hu01 纖溶酶原激活物抑制因子2(PAI2)多克隆抗體 Polyclonal Antibody to Plasminogen Activator Inhibitor 2 (PAI2)

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